Cor Triatriatum in an Adult with Late Presentation of Symptoms

[Cor triatriatum dexter of an adult].

Cor triatriatum dexter is a rare congenital malformation in which a membrane divides the right atrium into two chambers. The membrane represents a persistence of the right sinus venosus valve (RSV). Normally the RSV regresses between the 9th and 15th week of gestation, as the cephalic portion forms the crista terminalis and the caudal portion develops into the Eustachian and Thebesian valve. An...

Hemolytic anemia: an unusual presentation of cor triatriatum sinistrum.

Cor triatriatum is a congenital malformation of the heart which is usually presented with heart failure. We have dealt with an unusual presentation of a two-month-old child with cor triatriatum presented with hemolytic anemia.

Cor triatriatum masked by coexisting COPD in an adult.

Cor triatriatum presenting in adulthood is extremely rare. We describe a case of adult cor triatriatum in which the diagnosis was initially masked by the concomitant existence of COPD. Cardiac catheterization revealed only slightly elevated pulmonary wedge pressure despite severe pulmonary arterial hypertension. Both the primary lung disease and cor triatriatum greatly accentuated the pulmonary...

Cor triatriatum with pericardial agenesis.

Cor triatriatum sinister.

C triatriatum is a very rare congenital cardiac anomaly with no known associated genetic abnormalities. Cor triatriatum is generally an isolated anomaly but may be associated with anomalous pulmonary venous return in approximately 10% of patients, patent ductus arteriosus, left superior vena cava, ventricular septal defects, Shone syndrome, tricuspid atresia, Ebstein malformation, atrioventricu...